Rare Presentation of Mucous Membrane Pemphigoid With Pemphigoid of the Pulmonary System in 10-Month-Old Female

Authors

Hannah Kovar, LSU Health Sciences Center - New OrleansFollow
Ira Shukla, Children's Hospital of New Orleans, New Orleans, LA
India Hill, LSU Health Sciences Center - New OrleansFollow
Ty Theriot, LSU Health Sciences Center - New OrleansFollow
Gina Johnson, Skin Pathology Associates, Birmingham, AL
David V. Swetland, Children's Hospital of New Orleans, New Orleans, LA
Kayla B. Phelps, LSU Health Sciences Center - New OrleansFollow

Document Type

Article

Publication Date

11-18-2025

Publication Title

Pediatric Dermatology

Abstract

We present a 10-month-old girl with diffuse mucous membrane pemphigoid (MMP) and pemphigoid of the pulmonary system (POPS). Systemic corticosteroids, intravenous immunoglobulin, cyclophosphamide, rituximab, and mycophenolate mofetil led to improvement in cutaneous and mucosal lesions. However, she had progressively worsening airway involvement refractory to immunosuppression and ultimately died from respiratory failure.

PubMed ID

41254890

Rights

© 2025 Wiley Periodicals LLC

Recommended Citation

Kovar, Hannah; Shukla, Ira; Hill, India; Theriot, Ty; Johnson, Gina; Swetland, David V.; and Phelps, Kayla B., "Rare Presentation of Mucous Membrane Pemphigoid With Pemphigoid of the Pulmonary System in 10-Month-Old Female" (2025). School of Medicine Faculty Publications. 4302.
https://digitalscholar.lsuhsc.edu/som_facpubs/4302
10.1111/pde.70078