Unilateral hemicraniectomy with titanium cranioplasty for the treatment of high intracranial pressure in a pediatric patient with Camurati-Engelmann disease: illustrative case

Authors

Roboan Guillen-Arguello, LSU Health Sciences Center - New OrleansFollow
Nicholas Sader, University of Oklahoma College of Medicine
J. Gordon McComb, Keck School of Medicine of USC

Document Type

Article

Publication Date

12-16-2024

Publication Title

Journal of Neurosurgery: Case Lessons

Abstract

BACKGROUND Camurati-Engelmann disease (CED) is an extremely rare autosomal dominant genetic disorder that can cause increased intracranial pressure (ICP) secondary to cranial hyperostosis, which decreases intracranial volume. Surgical procedures to reduce ICP in medically refractory cases include intracranial volume expansion and ventriculoperitoneal shunting. OBSERVATIONS The authors present the case of a pediatric patient with CED and medically refractory increased ICP who underwent unilateral hemicraniectomy with titanium cranioplasty, resulting in a complete long-term resolution of symptoms. LESSONS Unilateral hemicraniectomy with titanium cranioplasty is a feasible surgical treatment for CED in pediatric patients with medically refractory increased ICP and papilledema.

PubMed ID

39680872

Volume

8

Issue

25

Creative Commons License

This work is licensed under a Creative Commons Attribution-NonCommercial-No Derivative Works 4.0 International License.

Recommended Citation

Guillen-Arguello, Roboan; Sader, Nicholas; and McComb, J. Gordon, "Unilateral hemicraniectomy with titanium cranioplasty for the treatment of high intracranial pressure in a pediatric patient with Camurati-Engelmann disease: illustrative case" (2024). School of Medicine Faculty Publications. 3303.
https://digitalscholar.lsuhsc.edu/som_facpubs/3303
10.3171/CASE24590